Giant right atrial thrombus in Noonan syndrome combined with Eisenmenger's complex.
نویسندگان
چکیده
A 54-year-old woman with the Noonan syndrome was admitted with congestive heart failure and a giant right atrial thrombus with atrial septal defect detected by two-dimensional echocardiography. The thrombus vanished on oral anticoagulant therapy with warfarin. The thrombus is considered to result from hemostasis in the right atrium due to congestive heart failure and to her specific skeletal characteristics. This report describes the first case of Noonan syndrome with right atrial thrombus.
منابع مشابه
Holt-Oram Syndrome: A Rare Variant
Holt-Oram syndrome is an autosomal dominant disorder, characterised by skeletal abnormalities of the upper limb associated with congenital heart defect, mainly atrial and ventricular septal defects. Skeletal defects exclusively affect the upper limbs in the preaxial radial ray distribution and are bilateral and asymmetrical. They range from clinodactyly, absent or digitalised thumb, hypoplastic...
متن کاملMassive pulmonary artery thrombosis with haemoptysis in adults with Eisenmenger's syndrome: a clinical dilemma.
Although the frequency of haemoptysis in Eisenmenger's syndrome is well recognised, the high prevalence of pulmonary artery thrombus has been newly appreciated through the growing use of non-invasive imaging. Three patients with Eisenmenger's syndrome with haemoptysis are reported who underwent computed tomography pulmonary angiography and cardiovascular magnetic resonance. Each patient was fou...
متن کاملAmiodarone-induced thyrotoxicosis in a case of Eisenmenger's syndrome.
Eisenmenger's syndrome is a condition due to any congenital heart defect with an intracardiac left-to-right communication that leads to pulmonary hypertension with reversed right-to-left blood flow and secondary cyanosis. The main complications of Eisenmenger's syndrome are heart failure and arrhythmias. Amiodarone, the drug of choice for arrhythmia treatment in such patients, can cause a numbe...
متن کاملSuccessful Pregnancy in a Patient with Eisenmenger's Syndrome (atrial Septal Defect with Shunt Reversal ).
MAUDE ABBOTT (1936) stated that the term Eisenmenger complex was used by her, for want of a better, to designate an unusual combination of VSD with dextroposition of the aorta without pulmonary stenosis or hypoplasia-first diagnosed during life by Von Schrotter and reported by Eisenmenger (1897). Wood (1950) suggested that pulmonary hypertension with reversed aorto-pulmonary, interventricular o...
متن کاملHeart failure in a patient with Noonan syndrome.
A 53-year-old man was admitted to our center with dyspnea and peripheral edema compatible with cardiac failure. His history was notable for Noonan syndrome, but he had not been seen a physician for 15 years. On examination, pectus excavatum, pectus carinatum, and low implantation of the ears were present (Figure 1). Blood pressure was 145/ 70 mm Hg, and pulse was irregular at 90 to 100 beats pe...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Chest
دوره 95 4 شماره
صفحات -
تاریخ انتشار 1989